| CASE REPORT |
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| Year : 2019 | Volume
: 24
| Issue : 1 | Page : 75-77 |
Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature
Hinglaj Saha1, Ghosh Tapanjyoti1, Somak Biswas1, Prafulla Kumar Mishra1, Kalyani Saha Basu1, Uttara Chatterjee2
1 Department of Paediatric Surgery, Nil Ratan Sircar Medical College and Hospital, Kolkata, West Bengal, India
2 Department of Pathology, IPGMER Medical College and Hospital, Kolkata, West Bengal, India
Correspondence Address:
Dr. Kalyani Saha Basu
B 2/4, Ananda Apartment, 44/1, A J Mistri Lane, Kolkata - 700 027, West Bengal
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/jiaps.JIAPS_235_17
Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2 PFIC.
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